Page 12 - PowerPoint Presentation

Associated Disorders

 Congenital hemangioma

Fully grown at birth. It has two clinical

forms

RICH: Rapidly involuting congenital

hemangioma. It involutes and

disappears at the first year of age

NICH: Non-involuting congenital

hemangioma. It dose not involute or

respond to pharmacotherapy. Surgery

may be offered if complications

develop

 Kaposifrom hemangioendothelioma / tufted

angioma

It is a locally aggressive tumour with a low

propensity to metastasis. It is usually > 5cm

in dimension. More than 50% is associated

with Kasabach-Merritt phenomenon.

Treatment options include corticosteroids

and surgery

 Other associated disorders

 Maffucci’s syndrome, von-Hippel-Lindau

syndrome, PHACE syndrome and epithelioid
hemangioma